Vasculo-Behçet’s Disease with Intra-Cardiac Mass, Pulmonary Artery Thrombus, and Pulmonary Artery Aneurysms

Behçet’s disease is a multi-system, inflammatory disorder with various clinical presentations. Vascular manifestations include arterial and venous thrombosis, aneurysms, and thrombophlebitis. Intra-cardiac mass is a rare presentation and is histologically composed of inflammatory cells, fibrosis, and thrombus. Treatment of vasculo-Behçet’s disease includes immune suppression, with consideration of anticoagulation depending upon the risk of bleeding from aneurysms. Invasive procedures should be deferred in patients with vasculo-Behçet’s disease because of the increased risk of aneurysm formation. We present a case of vasculo-Behçet’s disease complicated by intra-cardiac mass, pulmonary artery aneurysms, and pulmonary artery thrombus while providing a review of the variations in presentation, clinical outcomes, and management of vasculoBehçet’s disease in context with existing literature.